Phenylketonuria adults diet

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July 8, 2019
phenylketonuria adults diet

For older children and adults, the diet includes many fruits and vegetables. It also includes some low-protein breads, pastas and cereals.

Lipid status and long-chain polyunsaturated fatty acid concentrations in adults and adolescents with phenylketonuria on phenylalanine-restricted diet.

Adults with pku who have stopped the pku diet in their teens may benefit from a visit with their doctors. Returning to the diet may improve mental functioning and behavior and slow damage to the central nervous system that can result from high phenylalanine levels.

Protect a developing brain from high blood phenylalanine (phe) levels.

Many adults with pku find they function best while on a low-protein diet. The current advice is for people with pku to remain on a low-protein diet for life. Unlike in young children, there is not yet any evidence that high phenylalanine levels cause any permanent brain damage in adults with pku.

Many young adults have restarted the diet and found improvement in mental clarity as a result of lowered blood phenylalanine levels. Because phenylalanine occurs in practically all natural proteins, it is impossible to adequately restrict the diet using natural foods alone without compromising health.

В  treatment for pku normally involves a phenyalanine-restricted diet that is monitored carefully. Some children and adults with pku may be helped by the medication sapropterin in combination with a low-phenylalanine diet. Adults with high phenylalanine levels despite treatment may be helped by the medication pegvaliase.

Children and adults also need to avoid certain other foods and beverages, including many diet sodas and other drinks that contain aspartame (nutrasweet, equal). Aspartame is an artificial sweetener made with phenylalanine. Some medications may contain aspartame and some vitamins or other supplements may contain amino acids or skim milk powder.

Pku what is pku? Pku (phenylketonuria) is an inherited metabolic disorder caused by a deficiency of the enzyme phenylalanine hydroxylase (pah). In the united states, pku occurs in 1 in 10,000 to 1 in 15,000 newborn babies, according to the national human genome research institute.

Adults with uncontrolled high concentrations of pku can be treated the medication pegvaliase-pqpz (palynziq) to help reduce levels.